Intestinal Cystic Lymphangioma as an Uncommon Cause of Intussusception in an Infant: A Case Report
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Keywords
Lymphangioma Cystic, Intussusception, Intestinal Obstruction, Infant, Intestinal Resection
Abstract
Lymphangiomas are benign lymphatic vascular malformations; approximately 80% are diagnosed before 6 years of age. Intra-abdominal locations are rare and may present with obstruction, occasionally serving as a lead point for intussusception. Case presentation: A 15-month-old girl presented with a 24-hour history of intestinal obstruction, vomiting, hypoactive bowel sounds, and peritoneal irritation. Abdominal radiography showed an obstructive pattern. Exploratory laparotomy revealed an intussusception whose lead point was an intestinal cystic lymphangioma. Segmental intestinal resection with primary anastomosis was performed. Discussion: Intra-abdominal (mesenteric/intestinal) cystic lymphangioma is rare in pediatrics and can function as a pathological lead point for intussusception. Complete excision of the lesion with segmental resection, when indicated, is the treatment of choice and is usually associated with favorable outcomes. Conclusions: Cystic lymphangioma should be considered in the differential diagnosis of intussusception with a lead point in infants. Timely recognition and appropriate surgical management enable full resolution.
References
2. Alvite Canosa M, Alonso Fernández L, Seoane Vigo M, et al. Linfangioma quístico abdominal en una adolescente. Rev Esp Enferm Dig. 2008;100(8):515–22. Disponible en: https://scielo.isciii.es/scielo.php?script=sci_arttext&pid=S1130-01082008000800016
3. Ruiz Santiago ER, Rojas Concepción AA, Díaz Falcón Y. Quistes del mesenterio en niños como causa de abdomen agudo. Rev Cienc Méd. 2020;24(6):e4338. Disponible en: http://scielo.sld.cu/scielo.php?script=sci_arttext&pid=S1561-31942020000600018
4. Zagaceta Torres W, Ramírez García JF, Chávez Rosell MA. Linfangioma quístico de recto-sigmoides en un hospital público de Lima, Perú: reporte de caso. Rev Gastroenterol Peru. 2020;40(1):64–8. Disponible en: http://www.scielo.org.pe/scielo.php?script=sci_arttext&pid=S1022-51292020000100064
5. Kelley-Quon L, Arthur LG, Williams RF, et al. Management of intussusception in children: a systematic review. J Pediatr Surg. 2021;56(3):587–96. Disponible en: https://pubmed.ncbi.nlm.nih.gov/33158508/
6. Vo N, Sato T. Intususcepción en niños. Revisión de la literatura. UpToDate [Internet]. 2022. Disponible en: https://www.uptodate.com/contents/intussusception-in-children
7. Espinosa Arévalo M, Fernández Álvarez MB, Pérez Pedrosa A, et al. Linfangioma quístico mesentérico: a propósito de un caso de abdomen agudo. Rev Pediatr Aten Primaria. 2012;14:e1–14. Disponible en: https://scielo.isciii.es/scielo.php?script=sci_arttext&pid=S1139-76322012000300009
8. Kim SH, Kim HY, Lee C, et al. Clinical features of mesenteric lymphatic malformation in children. J Pediatr Surg. 2016;51(4):582–7. Disponible en: https://pubmed.ncbi.nlm.nih.gov/27106580/
9. Weeda VB, Booij KA, Aronson DC. Mesenteric cystic lymphangioma: a congenital and an acquired anomaly? Two cases and a review of the literature. J Pediatr Surg. 2008;43:1206–8. Disponible en: https://pubmed.ncbi.nlm.nih.gov/18558209/
10. Cabo RV, Suárez VJS, Villa VSG, et al. Mesenteric lymphangioma in the pediatric ages. Rev Cubana Pediatr. 2019;91(1):1–10. Disponible en: https://www.medigraphic.com/cgi-bin/new/resumenI.cgi?IDARTICULO=86021
11. Rojas CL, Molina GA. Lymphangioma cavernous of the small bowel mesentery: an infrequent cause of acute abdomen in adult. J Surg Case Rep. 2018;2018(2):1–3. Disponible en: https://pmc.ncbi.nlm.nih.gov/articles/PMC5811846/
12. Arago P, Alos R, Flors C, et al. Peritonitis due to a spontaneous rupture of a mesenteric cyst lymphangioma. Cir Esp. 2010;87(1):46–58. Disponible en: https://www.scielo.br/j/abcd/a/CK3JyKn8V87h4XbJysx8QCN/
13. Hamdi A, Nouri A, Selmi M, et al. Abdominal cystic lymphangioma in children. Ann Chir. 1993;47:553–6. Disponible en: https://pubmed.ncbi.nlm.nih.gov/8215185/
14. Piriz Momblant A, Figueras Torres B. Revisión sobre linfangioma quístico visceral: a propósito de tres casos. Rev Inf Cient. 2015;94(6):1427–40. Disponible en: https://revinfcientifica.sld.cu/index.php/ric/article/view/171/1429
15. García León L, Jaramillo Samaniego J, Véliz Lazo B. Abdomen agudo quirúrgico secundario a linfangioma quístico abdominal. Rev Med Hered. 2017;28:178–81. Disponible en: http://www.scielo.org.pe/scielo.php?script=sci_arttext&pid=S1018-130X2017000300007
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MD Luis Enrique Sánchez-Sierra, Universidad Nacional Autónoma de Honduras. Tegucigalpa, Honduras.
Médico residente de quinto año del Posgrado en Cirugía pediátrica
MD Arlin Ordoñez, Hospital Escuela. Tegucigalpa, Honduras
Médico especialista en Cirugía Pediátrica
MD Enrique Tome, Hospital Escuela. Tegucigalpa, Honduras
Médico especialista en Cirugía Pediátrica